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Test Price

1,800 AED

โœ… Home Collection Available

Sphingolipidosis Panel 1 Test in UAE | 1800 AED | DHA Licensed

Executive Summary & Core Metrics

Executive Summary

  • Accuracy Guarantee: 99.9% Diagnostic Sensitivity via ISO 9001:2015 Certified Processing.
  • Premium Logistics: VIP Mobile Phlebotomy & Temperature-Controlled Cold-Chain Home Collection (Available daily from 8 AM to 11 PM).
  • Clinical Guidance: Complimentary Telephonic Post-Test Clinical Result Interpretation.
  • Insurance: Direct Billing Verification via WhatsApp +971 54 548 8731

Test Overview & Methodology

The Sphingolipidosis Panel 1 is a high-precision enzymatic assay designed to screen for inborn errors of sphingolipid metabolism, including Gaucher, Fabry, and Niemann-Pick diseases. By measuring lysosomal enzyme activity in whole blood, this test provides early diagnostic clarity for neonates and pediatric patients, enabling timely multidisciplinary intervention.

Feature Our Sphingolipidosis Panel 1 Closest Alternative
Methodology Quantitative Fluorometric Enzyme Activity Assay (Gold Standard) Basic Colorimetric Enzyme Assay or Genetic Sequencing Only
Precision 99.9% Diagnostic Sensitivity, ISO-Validated Variable; often 85โ€“92% depending on lab
Turnaround Time 4 days (Sample by 4 pm daily) 7โ€“14 days

Physician Insight & Safety Protocols

โ€œAs a consultant medical geneticist, I emphasize that enzyme activity results must always be correlated with clinical phenotype and genetic findings. This panel offers a critical biochemical fingerprint, but a negative result does not entirely exclude sphingolipidosis if strong clinical suspicion persists. Multidisciplinary collaboration ensures optimal outcomes for every child.โ€

โ€” Lina Osama Zaki Quteineh, Consultant Medical Genetics | DHA Registration ID: 9294403

โš  Clinical Notice

Do not discontinue any prescribed medication or therapy based solely on this test outcome. Always consult your managing physician.

Safety Exclusion Criteria & Emergency Red Flags

  • Active systemic infection or sepsis โ€“ postpone collection until 14 days after clinical resolution.
  • Clotting disorders or anticoagulant therapy; require physician clearance prior to phlebotomy.
  • Inadequate sample volume (< 7.5 mL) or hemolysis; reject and recollect immediately.
  • Unrefrigerated sample exceeding 48-hour stability window; results will be cancelled.
  • ER Red Flag: If patient exhibits acute neurological deterioration, seizure, or loss of consciousness, proceed directly to Emergency Department โ€“ do not wait for test results.

Patient FAQ & Clinical Guidance

1. What does the Sphingolipidosis Panel 1 measure?

This enzymatic panel quantifies the activity of key lysosomal enzymes (e.g., glucocerebrosidase, alpha-galactosidase, sphingomyelinase) directly from whole blood to screen for Gaucher, Fabry, and Niemann-Pick diseases.

2. How long until results are available?

Results are reported within 4 working days after sample receipt by 4 pm daily, with optional immediate phone notification.

3. Is home blood collection safe for my baby?

Our DHA-licensed pediatric phlebotomists use ultra-fine gauge needles and adhere to strict ISO cold-chain protocols, with all necessary resuscitation equipment on boardโ€”ensuring a stress-minimized, hospital-grade home collection.

4. Does insurance cover this test?

We provide direct insurance coverage verification via WhatsApp at +971 54 548 8731 prior to collection, compliant with DHA regulations.

UAE Regulatory & Data Privacy Adherence

โœ… Federal Decree-Law No. 45 of 2021 on Personal Data Protection (PDPL)

โœ… Federal Law No. 2 of 2019 Concerning the Use of Information and Communication Technology in Health Fields

โœ… Federal Decree-Law No. 4 of 2016 on Medical Liability

ISO 9001:2015 Certified Facility | Cert: INT/EGQ/2509DA/3139 | DHA/MOHAP Licensed

Clinical & Logistical Metadata

Test Name Sphingolipidosis Panel 1 โ€“ Lysosomal Enzyme Activity Assay
Price (AED) 1,800 AED
Turnaround Time 4 working days (sample cut-off 4 pm daily)
Sample Type / Matrix Whole Blood (peripheral venous) โ€“ VIP Mobile Phlebotomy & Temperature-Controlled Cold-Chain Home Collection available daily 8 AM โ€“ 11 PM
Methodology Used Quantitative Fluorometric Enzyme Activity Assay (Gold Standard)
ICD-10-CM Code E75.2
LOINC Code 47828-9
DHA Facility License & Laboratory Address DHA License No: 1143 | Premises 105, Floor 1, Building 33, Dubai Healthcare City, Dubai, UAE | DNA Labs UAE

ุฏุนู… ุซู†ุงุฆูŠ ุงู„ู„ุบุฉ ู…ุชุงุญ

ุงู„ุชุญู‚ู‚ ู…ู† ุงู„ุชุบุทูŠุฉ ุงู„ุชุฃู…ูŠู†ูŠุฉ

Check Insurance Coverage Instantly

Stop the guesswork. Send a photo of your Insurance Card and Doctor's Prescription to our DHA-Certified Verification Team on WhatsApp.

ุชูˆู‚ู ุนู† ุงู„ุชุฎู…ูŠู†. ุฃุฑุณู„ ุตูˆุฑุฉ ู…ู† ุจุทุงู‚ุฉ ุงู„ุชุฃู…ูŠู† ูˆูˆุตูุฉ ุงู„ุทุจูŠุจ ุฅู„ู‰ ูุฑูŠู‚ ุงู„ุชุญู‚ู‚ ุงู„ู…ุนุชู…ุฏ ู…ู† ู‡ูŠุฆุฉ ุงู„ุตุญุฉ ุจุฏุจูŠ ุนุจุฑ ุงู„ูˆุงุชุณุงุจ. ุงุญุตู„ ุนู„ู‰ ุชุญุฏูŠุซ ุงู„ุญุงู„ุฉ ููŠ ุฏู‚ุงุฆู‚.

โœ… DHA Certified โœ… ISO 15189 โœ… HIPAA Compliant

Available in Arabic, English, Hindi & Urdu

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ISMS 27001:2022

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ISO Accredited

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HIPAA

All reports reviewed by DHA-Certified physicians